Happy Monday.
Last quiz I asked you about a 4 month old baby with trisomy 21 and confirmed HD, who has been doing well on irrigations, with the below contrast study. Sometimes these quizzes can be straight forward and this was an example. Of the choices below,
I would recommend laparoscopy with biopsy of the proximal sigmoid (option 2) which looks good on the contrast study and then proceeding with a standard lap assisted plus transanal pull-through. Our biopsy in the upper sigmoid showed good ganglion cells and normal nerves.
For this week, I saw a 16 year old male with HD, previous redo pull-through for a retained cuff at age 11. He stools three times a day, somewhat soft consistency, and often has urgency, and occasionally has a soiling accident. He is not distended and has not had any episodes of enterocolitis since his redo. His contrast enema and plain abdominal xray is below. His exam showed no stricture and an intact dentate line, and no residual cuff. The biopsy at the time of the redo was normal.
What would you recommend for his treatment?
Here is the current list of the Colorectal Quiz podcasts, best viewed via the StayCurrent app:
Colorectal Quiz Episode 1 ARM - Low Bulbar Fistula, https://staycurrentapp.app.link/wK2FhonUEhb
Colorectal Quiz Episode 2 When to redo a PSARP https://staycurrentapp.app.link/RX2eeDqUEhb
Colorectal Quiz Episode 3 Hirschprung Disease https://staycurrentapp.app.link/UnFRkprUEhb
Colorectal Quiz Episode 3.5 Proximal Hirschsprung Disease https://staycurrentapp.app.link/JiaWCGsUEhb
Colorectal Quiz Episode 4 Classic Hirschsprung disease - Surgical Technique https://staycurrentapp.app.link/qGWLoGtUEhb
Colorectal Quiz Episode 5 Proximal Hirschsprung Disease Surgical Technique https://staycurrentapp.app.link/AiGHjcvUEhb
Colorectal Quiz Episode 6 Bowel Management Part 1 https://staycurrentapp.app.link/SVuVYWvUEhb
Colorectal Quiz Episode 7 Bowel Management Part 2 https://staycurrentapp.app.link/b8IhkKwUEhb
Colorectal Quiz Episode 8 Motility Disorders Part 1 https://staycurrentapp.app.link/NRerIoxUEhb
Colorectal Quiz Episode 9 Motility Disorders Part 2 https://staycurrentapp.app.link/s2cVlbyUEhb
Colorectal Quiz Episode 10 Total Colonic Hirschsprung Disease Part 1 https://staycurrentapp.app.link/fEtTMRyUEhb
Colorectal Quiz Episode 11 Total Colonic Hirschsprung's Part 2 https://staycurrentapp.app.link/MNqS9yzUEhb
Colorectal Quiz episode 12 Newborn ARM Part 1 https://staycurrentapp.app.link/x5UL6DBUEhb
Colorectal Quiz Episode 13 Newborn ARM Part 2 https://staycurrentapp.app.link/YqVpTmCUEhb
Colorectal Quiz Episode 14 ARM Newborn Part 3 https://staycurrentapp.app.link/x9mUY7CUEhb
Colorectal Quiz Episode 15 Bowel Management in Spinal Pts. Need for a urologist Part 1 https://staycurrentapp.app.link/etX3mPDUEhb
Colorectal Quiz Episode 16 Bowel Management in Spinal Pts. Need for a urologist Part 2 https://staycurrentapp.app.link/5C7GsJIDEhb
Colorectal Quiz Episode 17 Cloaca Part I https://staycurrentapp.app.link/YGPmYZPEPhb
Colorectal Quiz Episode 18 Cloaca Part II https://staycurrentapp.app.link/vUEzQxG80hb
Colorectal Quiz Episode 19 Hirschsprung Disease - The Obstructed Patient Part 1 https://staycurrentapp.app.link/gBzrAtLKLib
Colorectal Quiz: Episode 20 Hirschsprung Disease – The Obstructed Patient Part 2 https://staycurrentapp.app.link/W7kEcqB6vjb
Colorectal Quiz Episode 21 The History of Hirschsprung Disease https://staycurrentapp.app.link/QXtFg2UlTjb
Colorectal Quiz Episode 22 Hirschsprung Disease - the Soiling Patient Part 1 https://staycurrentapp.app.link/OII38hVhQkb
Colorectal Quiz Episode 23 Hirschsprung Disease The Soiling Patient Part 2 https://staycurrentapp.app.link/DA4WEDIcXlb
Colorectal Quiz Episode 24 Cloaca Part 3 https://staycurrentapp.app.link/3uuEG49mkmb
Colorectal Quiz Episode 25 Perineal Groove https://staycurrentapp.app.link/PxlGWtfswmb
Colorectal Quiz Episode 26 Perianal Crohn's Disease https://staycurrentapp.app.link/qQbadIDjTmb
Colorectal Quiz Episode 27: Delayed Hirschsprung Disease
https://staycurrentapp.app.link/v37xYPDSDnb
Colorectal Quiz Episode 28: Female ARM Management - Perineal Fistula https://staycurrentapp.app.link/lLH7KQr20nb
Colorectal Quiz Episode 30: Tethered Cord https://staycurrentapp.app.link/sE57H6IPzob
Colorectal Quiz Episode 31: Müllerian Anomalies in patients with ARM
https://staycurrentapp.app.link/FuQyrjuC8ob