Quiz for August 14:
For this week, a variation on the theme from last week, how would you approach this male ARM, with the below distal colostogram. I added the sacral x-ray because the sacrum is hard to see on the colostogram images.
Answer for August 14:
This is a tough one – PSARP would be hard – reaching this rectum is doable from below but the good rectum is above the coccyx. My preference here would be laparoscopy. There does appear to be an adequate amount of length from the mucous fistula. The sacrum is a bit short so that does help with posterior sagittal exposure.
Quiz for August 21:
A baby girl with ARM and rectovestibular fistula is taken to the OR for planned PSARP. Careful inspection reveal at first a normal appearing introitus and hymen, but probing shows that in fact she has distal vaginal atresia. What would you do in this case? Some potential options are below.
a. Cancel the procedure and come back another day
b. Proceed with PSARP and leave the vagina for another day
c. Proceed with PSARP and perform laparoscopy to determine the Mullerian anatomy
d. Proceed with PSARP and perform vaginal replacement using the distal rectum left for neovagina and mobilize a more proximal piece of rectum for the anoplasty
e. Proceed with PSARP using the rectum in the vestibule for rectum and performing a neovagina with sigmoid or small bowel
f. Something not listed above, in such a case I would________________________________.