Colorectal Quiz: March 13, 2023

Ron Reeder • March 13, 2023

The question from last week:

A newborn has intestinal obstruction with impressive abdominal distension This contrast study is performed and is read as small left colon syndrome (mom is a diabetic). Irrigations are started and don’t really help decompress the baby, and it has been a week and no real improvement. Hirschsprung disease is suspected and a suction biopsy at 2 cm shows ganglion cells with hypertrophic nerves. What do you think could be going on? What would you do?


Answer: The narrowed left colon guided the surgeons down the wrong path, it was in fact normal. The rectal biopsy was normal, there was no Hirschsprung disease. Smartly the surgeon decided to explore the patient and found an ileal atresia which was repaired with a primary anastomosis. 


For this week: 

I received a query about a female patient born with imperforate anus. At birth, no anus was identified and on exploration to perform a colostomy, a pouch colon was found (colonic atresia). Due to the dilation of the colonic segment, the surgeons chose to resect it and perform an ileostomy. Thereafter an ileoanal pull-through was performed. The child is now 3 years of age. She suffers from severe perianal excoriation. The contrast study is shown. What would you recommend be done for this child?

How would you handle this case?

New Paragraph

By Ron Reeder January 29, 2024
Colorectal Conundrum for January 29: A male with a rectoperineal fistula undergoes a PSARP with mobilization of the rectum, both anterior and posterior rectal walls. In the days following surgery he starts to drain urine around the anoplasty consistent with a urethral injury. He is also voiding via the penis. A cystogram is shown below. How would you manage this situation? Answer: This patient has suffered from a urethral injury, and urine is draining out the posterior urethra into the perineum around the anoplasty. The key first step is to divert the urine with a suprapubic tube. A colostomy is not necessarily needed. The fistula might heal with diversion. If after a month or so a cystogram shows the persistence of the fistula, then a redo is needed with re-mobilization of the rectum, fully lifting the anterior rectal wall off of the urinary tract, and repair the urethra, with coverage of the posterior urethra with an ischiorectal fat pad. Then a voiding trial a month later with ultimate removal of the SP tube.
By Ron Reeder January 22, 2024
Colorectal Conundrum for January 22nd: In the previous week’s case, of an imperforate hymen, the MRI showed dilation all the way down to the perineum. Management involved a perineal – introital – incision to drain the fluid. If that were not the case and you had a dilated vagina but the distal extent was far away from the introital area, how might you handle that hydrocolpos? Answer: If this were a case of hydrolpos with normal anus and normal urethra, and the vagina cannot be drained by the introitus like an imperforate hymen, then drainage needs to be from above. IR or laparoscopy is an ideal approach to get a drain in the dilated structure (remember this could be bilateral, so both sides may need to be drained. Drainage is to relieve distension and most concerning its potential cause of distal ureteral obstruction causing hydronephrosis. Once the material hormones have dissipated the hydrocolpos will resolve and can be dealt with later in life via a laparoscopic distal vaginal pull-through, after the onset of puberty. In such a patient, I would follow closely with ultrasound 6 months after thelarche (breast budding).
By Ron Reeder January 16, 2024
Colorectal Conundrum for January 16: A newborn female is noted to have abdominal distension. On exam the uretha and anus are normal, and there appears to be a bulge in the hymen. The has an MRI with the image shown below. What would be your treatment plan? What are the variations in such a case and how would you manage each? Answer: This could be a case of imperforate hymen, but the MRI is key – how high up is the obstruction? How large is the hydrocolpos? In this case, it appears that a perineal incision might all that is needed as the dilation extends all the way down to the perineum. That is the most common scenario. An incision at the level of the hymen should drain out the fluid and no further intervention should be needed. Of course a careful exam needs to check to be certain you see a urethra – sometimes such a bulge could be a paraurethral cyst. For the next week’s question – what would you do if the perineal approach was inadequate – i.e. could not reach the dilated lumen.
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