Happy Monday all. This quiz will need to last you for two weeks as I am away next Monday.
Last week I asked you about a case sent to us by Dr. Mansur Nasirov, from Tashkent. Uzbekistan of a 1 year old male with a rectovesical fistula, atrial septal defect, and bilateral vesicoureteral reflux, who had a colostomy at birth. Below is the distal colostogram.
This case demonstrates a distal segment that is short, either because the sigmoid didn’t have much of a curve or because the surgeon who referred the patient to Dr. Nasirov made the stoma too distal in the sigmoid. I would try hard to save the rectum, and would mobilize the distal rectum via laparoscopy or laparotomy. This piece of rectum will only reach if you also take down the mucous fistula, and I would definitely not want to leave a Hartman’s pouch behind the bladder – which would make the colostomy closure very difficult. So to help with that situation you could close the colostomy at the same time, and then open up either a more proximal colostomy or an ileostomy. Another option as several of you suggested is to leave the patient undiverted.
For this week, I am curious what you would recommend for an 11 year old boy we saw with chronic distension and constipation, with several failure to thrive. An anorectal manometry failed to demonstrate a RAIR, but the rectal biopsy did show ganglion cells – so no Hirschsprung disease. The colon is massively distended on plain xray and on contrast study with no area of obstruction.
Here is the current list of the Colorectal Quiz podcasts, best viewed via the StayCurrent app:
Colorectal Quiz Episode 1 ARM - Low Bulbar Fistula, https://staycurrentapp.app.link/wK2FhonUEhb
Colorectal Quiz Episode 2 When to redo a PSARP https://staycurrentapp.app.link/RX2eeDqUEhb
Colorectal Quiz Episode 3 Hirschprung Disease https://staycurrentapp.app.link/UnFRkprUEhb
Colorectal Quiz Episode 3.5 Proximal Hirschsprung Disease https://staycurrentapp.app.link/JiaWCGsUEhb
Colorectal Quiz Episode 4 Classic Hirschsprung disease - Surgical Technique https://staycurrentapp.app.link/qGWLoGtUEhb
Colorectal Quiz Episode 5 Proximal Hirschsprung Disease Surgical Technique https://staycurrentapp.app.link/AiGHjcvUEhb
Colorectal Quiz Episode 6 Bowel Management Part 1 https://staycurrentapp.app.link/SVuVYWvUEhb
Colorectal Quiz Episode 7 Bowel Management Part 2 https://staycurrentapp.app.link/b8IhkKwUEhb
Colorectal Quiz Episode 8 Motility Disorders Part 1 https://staycurrentapp.app.link/NRerIoxUEhb
Colorectal Quiz Episode 9 Motility Disorders Part 2 https://staycurrentapp.app.link/s2cVlbyUEhb
Colorectal Quiz Episode 10 Total Colonic Hirschsprung Disease Part 1 https://staycurrentapp.app.link/fEtTMRyUEhb
Colorectal Quiz Episode 11 Total Colonic Hirschsprung's Part 2 https://staycurrentapp.app.link/MNqS9yzUEhb
Colorectal Quiz episode 12 Newborn ARM Part 1 https://staycurrentapp.app.link/x5UL6DBUEhb
Colorectal Quiz Episode 13 Newborn ARM Part 2 https://staycurrentapp.app.link/YqVpTmCUEhb
Colorectal Quiz Episode 14 ARM Newborn Part 3 https://staycurrentapp.app.link/x9mUY7CUEhb
Colorectal Quiz Episode 15 Bowel Management in Spinal Pts. Need for a urologist Part 1 https://staycurrentapp.app.link/etX3mPDUEhb
Colorectal Quiz Episode 16 Bowel Management in Spinal Pts. Need for a urologist Part 2 https://staycurrentapp.app.link/5C7GsJIDEhb
Colorectal Quiz Episode 17 Cloaca Part I https://staycurrentapp.app.link/YGPmYZPEPhb
Colorectal Quiz Episode 18 Cloaca Part II https://staycurrentapp.app.link/vUEzQxG80hb
Colorectal Quiz Episode 19 Hirschsprung Disease - The Obstructed Patient Part 1 https://staycurrentapp.app.link/gBzrAtLKLib
Colorectal Quiz: Episode 20 Hirschsprung Disease – The Obstructed Patient Part 2 https://staycurrentapp.app.link/W7kEcqB6vjb
Colorectal Quiz Episode 21 The History of Hirschsprung Disease https://staycurrentapp.app.link/QXtFg2UlTjb
Colorectal Quiz Episode 22 Hirschsprung Disease - the Soiling Patient Part 1 https://staycurrentapp.app.link/OII38hVhQkb
Colorectal Quiz Episode 23 Hirschsprung Disease The Soiling Patient Part 2 https://staycurrentapp.app.link/DA4WEDIcXlb
Colorectal Quiz Episode 24 Cloaca Part 3 https://staycurrentapp.app.link/3uuEG49mkmb
Colorectal Quiz Episode 25 Perineal Groove https://staycurrentapp.app.link/PxlGWtfswmb
Colorectal Quiz Episode 26 Perianal Crohn's Disease https://staycurrentapp.app.link/qQbadIDjTmb
Colorectal Quiz Episode 27: Delayed Hirschsprung Disease https://staycurrentapp.app.link/v37xYPDSDnb
Colorectal Quiz Episode 28: Female ARM Management - Perineal Fistula https://staycurrentapp.app.link/lLH7KQr20nb
Colorectal Quiz Episode 30: Tethered Cord https://staycurrentapp.app.link/sE57H6IPzob
Some announcements of future meetings – please join for these virtual offerings by the pcplc.